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Allison Gregory Selected Research

Pantothenate Kinase-Associated Neurodegeneration (Hallervorden-Spatz Disease)

12/2021Consensus clinical management guideline for beta-propeller protein-associated neurodegeneration.
1/2020Magnetic resonance imaging pattern recognition in childhood bilateral basal ganglia disorders.
1/2017Changes in Red Blood Cell membrane lipid composition: A new perspective into the pathogenesis of PKAN.
12/2015Pallidal neuronal apolipoprotein E in pantothenate kinase-associated neurodegeneration recapitulates ischemic injury to the globus pallidus.
11/2013Metabolism and energy requirements in pantothenate kinase-associated neurodegeneration.
6/2011Genetics of neurodegeneration with brain iron accumulation.
4/2011Novel histopathologic findings in molecularly-confirmed pantothenate kinase-associated neurodegeneration.
1/2005Neurodegeneration with brain iron accumulation.

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Allison Gregory Research Topics

Disease

8Pantothenate Kinase-Associated Neurodegeneration (Hallervorden-Spatz Disease)
12/2021 - 01/2005
7Neurodegeneration with brain iron accumulation (NBIA)
01/2017 - 01/2005
4Neurodegenerative Diseases (Neurodegenerative Disease)
12/2021 - 07/2006
3Parkinsonian Disorders (Parkinsonism)
12/2020 - 06/2013
3Inborn Genetic Diseases (Disease, Hereditary)
01/2020 - 07/2006
3Movement Disorders (Movement Disorder)
01/2013 - 04/2011
2Neuroaxonal Dystrophies (Neuroaxonal Dystrophy, Late Infantile)
12/2021 - 07/2006
2Dystonia (Limb Dystonia)
12/2020 - 01/2016
2Basal Ganglia Diseases (Basal Ganglia Disease)
01/2020 - 01/2005
1Epilepsy (Aura)
12/2021
1Fatty Acid Hydroxylase-Associated Neurodegeneration
12/2021
1Lymphatic Metastasis
11/2021
1Melanoma (Melanoma, Malignant)
11/2021
1Dysphonia (Spastic Dysphonia)
12/2020
1Kernicterus
01/2020
1succinic semialdehyde dehydrogenase deficiency
01/2020
13-Methylglutaconic Aciduria
01/2020
1Brain Diseases (Brain Disorder)
01/2020
1Cerebral Palsy (Spastic Diplegia)
01/2020
1Deafness (Deaf Mutism)
01/2020
1Kearns-Sayre Syndrome
01/2020
1Globoid Cell Leukodystrophy (Krabbe Disease)
01/2020
1Pyruvate Dehydrogenase Complex Deficiency Disease
01/2020
1Dystonic Disorders (Writer's Cramp)
12/2016
1Optic Atrophy
12/2016
1Infarction (Infarctions)
12/2015
1Atypical Rett Syndrome
03/2015
1Dyskinesias (Dyskinesia)
06/2013
1Dementia (Dementias)
01/2013
1Cognitive Dysfunction
01/2013
1Karak Syndrome
07/2006
1Parkinson Disease (Parkinson's Disease)
07/2006
1Alzheimer Disease (Alzheimer's Disease)
07/2006

Drug/Important Bio-Agent (IBA)

12IronIBA
12/2021 - 01/2005
4Proteins (Proteins, Gene)FDA Link
12/2021 - 01/2013
2pantothenate kinaseIBA
01/2017 - 11/2013
2Coenzyme A (CoA)IBA
11/2013 - 01/2005
1NivolumabIBA
11/2021
1Thiamine (Aneurin)FDA Link
01/2020
1VigabatrinFDA Link
01/2020
1Fatty Acids (Saturated Fatty Acids)IBA
12/2016
1ManganeseIBA
01/2016
1Aminobutyrates (Aminobutyric Acid)IBA
12/2015
1ApolipoproteinsIBA
12/2015
1gamma-Aminobutyric Acid (GABA)IBA
12/2015
1UbiquitinIBA
12/2015
1Levodopa (L Dopa)FDA LinkGeneric
06/2013
1Phospholipases A2 (Phospholipase A2)IBA
07/2006
1CalciumIBA
07/2006
1Phospholipases (Phospholipase)IBA
07/2006
1Group VI Phospholipases A2IBA
07/2006

Therapy/Procedure

1Deep Brain Stimulation
12/2020